{"id":3480,"date":"2024-03-07T11:43:27","date_gmt":"2024-03-07T03:43:27","guid":{"rendered":"https:\/\/imbhg.tcu.edu.tw\/?p=3480"},"modified":"2024-03-07T11:51:49","modified_gmt":"2024-03-07T03:51:49","slug":"%e3%80%8c%e8%ab%be%e5%81%a5%e7%94%9f%e3%80%8d%e7%b4%8d%e5%85%a5%e5%81%a5%e4%bf%9d%e7%b5%a6%e4%bb%98%ef%bc%9a%e7%bd%95%e8%a6%8b%e7%96%be%e7%97%85%e5%9f%ba%e5%9b%a0%e6%b2%bb%e7%99%82%e6%96%b0%e9%87%8c","status":"publish","type":"post","link":"https:\/\/imbhg.tcu.edu.tw\/?p=3480","title":{"rendered":"\u300c\u8afe\u5065\u751f\u300d\u7d0d\u5165\u5065\u4fdd\u7d66\u4ed8\uff1a\u7f55\u898b\u75be\u75c5\u57fa\u56e0\u6cbb\u7642\u65b0\u91cc\u7a0b\u7891\uff01"},"content":{"rendered":"<p><img loading=\"lazy\" decoding=\"async\" class=\"size-medium wp-image-3481 aligncenter\" src=\"https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/1-300x300.jpg\" alt=\"\" width=\"300\" height=\"300\" srcset=\"https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/1-300x300.jpg 300w, https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/1-150x150.jpg 150w, https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/1-768x768.jpg 768w, https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/1-375x375.jpg 375w, https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/1.jpg 1024w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/p>\n<p style=\"text-align: right;\">\u5716\/\u6587 \u5f35\u65b0\u4faf\u6559\u6388<\/p>\n<p>\u62531\u529149000\u842c\uff01\u5168\u7403\u6700\u8cb4\u85e5\u7269\u4e4b\u4e00\u300c\u8afe\u5065\u751f\u300d (Zolgensma)\uff0c\u6cbb\u7642\u7f55\u898b\u75be\u75c5\u810a\u9ad3\u808c\u8089\u840e\u7e2e\u75c7(Spinal Muscular 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neuron)\u57fa\u56e0\u7f3a\u640d\uff0c\u5c0e\u81f4\u810a\u9ad3\u7684\u524d\u89d2\u7d30\u80de\uff08\u904b\u52d5\u795e\u7d93\u5143\uff09\u9000\u5316\uff0c\u9020\u6210\u808c\u8089\u7121\u529b\u53ca\u840e\u7e2e\u7684\u4e00\u7a2e\u9ad4\u96b1\u6027\u907a\u50b3\u7f55\u898b\u75be\u75c5\u3002\u60a3\u8005\u5f80\u5f80\u5728\u5e7c\u5e74\u6642\u671f\u51fa\u73fe\u75c7\u72c0\uff0c\u00a0\u5728\u4e16\u754c\u5404\u570b\u810a\u9ad3\u808c\u8089\u840e\u7e2e\u75c7\u767c\u751f\u7387\u7d04\u70ba1\/10000\uff0c\u4e5f\u5c31\u662f\u8aaa\u53f0\u7063\u6bcf\u5e74\u51fa\u751f\u7684\u65b0\u751f\u5152\u7576\u4e2d\u7d04\u670925\u500b\u7f79\u60a3\u6b64\u75c7\uff0c\u662f\u4e16\u754c\u4e0a\u907a\u50b3\u6027\u75be\u75c5\u4e2d\u9020\u6210\u5b30\u5152\u6b7b\u4ea1\u7387\u6700\u9ad8\u7684\u75be\u75c5\u3002\u8afe\u5065\u751f\u7684\u7d0d\u5165\u5065\u4fdd\u7d66\u4ed8\uff0c\u610f\u5473\u8457\u53f0\u7063SMA\u60a3\u8005\u5c07\u80fd\u5920\u7372\u5f97\u66f4\u70ba\u5168\u9762\u548c\u6709\u6548\u7684\u6cbb\u7642\uff0c\u9019\u662f\u4e00\u500b\u91cd\u5927\u7684\u91ab\u7642\u9032\u6b65\uff0c\u4e5f\u662f\u5c0d\u7f55\u898b\u75be\u75c5\u60a3\u8005\u6b0a\u76ca\u7684\u4fdd\u969c\u3002<\/p>\n<p>\u8afe\u5065\u751f\u662f\u4e00\u7a2e\u300c\u57fa\u56e0\u6cbb\u7642\u300d\u85e5\u7269\uff0c\u70ba\u4e00\u7a2e\u8a2d\u8a08\u5c07\u904b\u52d5\u795e\u7d93\u5143\u5b58\u6d3b1\u57fa\u56e0(SMN1)\u7684\u529f\u80fd\u6027\u62f7\u8c9d\u5c0e\u5165\u8f49\u5c0e\u7d30\u80de\u4e2d\u7684\u57fa\u56e0\u7642\u6cd5\uff0c\u89e3\u6c7a\u8a72\u75be\u75c5\u7684\u55ae\u57fa\u56e0\u6839\u672c\u6210\u56e0\u3002\u5b83\u7684\u7368\u7279\u4e4b\u8655\u5728\u65bc\u4e00\u6b21\u6ce8\u5c04\u7d42\u8eab\u6709\u6548\uff0c\u76f8\u8f03\u65bc\u50b3\u7d71\u7684\u6cbb\u7642\u65b9\u5f0f\uff0c\u5982\u810a\u745e\u62c9\u6ce8\u5c04\u6db2\u548c\u670d\u810a\u7acb\u53e3\u670d\u6eb6\u6db2\u7528\u7c89\u5291\uff0c\u8afe\u5065\u751f\u70ba\u60a3\u8005\u5e36\u4f86\u66f4\u4fbf\u6377\u548c\u6709\u6548\u7684\u6cbb\u7642\u65b9\u6848\u3002\u5065\u4fdd\u7f72\u91dd\u5c0d\u8afe\u5065\u751f\u7684\u4ed8\u6b3e\u65b9\u5f0f\u9032\u884c\u4e86\u7d30\u81f4\u7684\u8003\u91cf\uff0c\u63a1\u53d6\u5206\u671f\u4ed8\u6b3e\u7684\u65b9\u5f0f\uff0c\u4ee5\u6e1b\u8f15\u60a3\u8005\u5bb6\u5ead\u7684\u8ca0\u64d4\uff0c\u540c\u6642\u78ba\u4fdd\u75c5\u60a3\u80fd\u5920\u6301\u7e8c\u63a5\u53d7\u6cbb\u7642\u3002\u85c9\u7531\u6b64\u8209\uff0c\u5065\u4fdd\u7f72\u5c55\u73fe\u4e86\u5c0d\u65bc\u7f55\u898b\u75be\u75c5\u60a3\u8005\u751f\u547d\u50f9\u503c\u7684\u5c0a\u91cd\uff0c\u4ee5\u53ca\u5c0d\u65bc\u91ab\u7642\u79d1\u6280\u767c\u5c55\u7684\u7a4d\u6975\u61c9\u5c0d\uff0c\u70ba\u53f0\u7063\u7684\u91ab\u7642\u4fdd\u969c\u9ad4\u7cfb\u6ce8\u5165\u4e86\u65b0\u7684\u6d3b\u529b\u3002<\/p>\n<p>\u6148\u6fdf\u5927\u5b78\u5206\u5b50\u751f\u7269\u66a8\u4eba\u985e\u907a\u50b3\u5b78\u7cfb\u7684\u5b78\u751f\u5c07\u53d7\u76ca\u65bc\u9019\u4e00\u91cd\u5927\u6a5f\u6703\u3002\u672c\u7cfb\u6b63\u662f\u53f0\u7063\u76ee\u524d\u552f\u4e00\u4ee5\u5206\u5b50\u751f\u7269,\u4eba\u985e\u907a\u50b3\u53ca\u57fa\u56e0\u6280\u8853\u70ba\u4e3b\u8981\u5b78\u7fd2\u6a19\u7684\u7684\u5b78\u7cfb\uff0c\u5927\u5b78\u7684\u8ab2\u7a0b\u898f\u5283\u57fa\u56e0\u79d1\u6280\u5b78\u7fa4\uff0c\u78a9\u58eb\u73ed\u6709\u907a\u50b3\u8aee\u8a62\u5e2b\u5b78\u7fa4\uff0c\u5c08\u9580\u8ab2\u7a0b\u8b1b\u89e3\u5404\u7a2e\u7f55\u898b\u75be\u75c5\uff0c\u4ee5\u53ca\u300c\u57fa\u56e0\u6cbb\u7642\u300d\u7684\u539f\u7406\u8207\u5be6\u969b\u61c9\u7528\u3002\u4e26\u9577\u671f\u95dc\u6ce8\u7f55\u898b\u75be\u75c5\u75c5\u53cb\u7684\u9700\u6c42\u3002\u6b64\u5916\uff0c\u672c\u7cfb\u7684\u540c\u5b78\u5c07\u6709\u6a5f\u6703\u6df1\u5165\u4e86\u89e3\u57fa\u56e0\u6cbb\u7642\u6280\u8853\u7684\u5be6\u969b\u61c9\u7528\uff0c\u53c3\u8207\u76f8\u95dc\u7814\u7a76\uff0c\u70ba\u7f55\u898b\u75be\u75c5\u60a3\u8005\u7684\u6cbb\u7642\u8ca2\u737b\u81ea\u5df1\u7684\u529b\u91cf\u3002\u8eab\u8655\u65bc\u57fa\u56e0\u6280\u8853\u5c08\u696d\u9818\u57df\u7684\u5b78\u751f\u5011\uff0c\u5c07\u80fd\u5920\u7a4d\u6975\u53c3\u8207\u6b64\u6b21\u91cc\u7a0b\u7891\u4e8b\u4ef6\u7684\u8a0e\u8ad6\u548c\u7814\u7a76\uff0c\u70ba\u793e\u6703\u798f\u7949\u548c\u79d1\u6280\u767c\u5c55\u505a\u51fa\u66f4\u591a\u7684\u8ca2\u737b\u3002\u9019\u4e00\u91cd\u5927\u9032\u5c55\u63d0\u9192\u6211\u5011\uff0c\u5c0d\u65bc\u7f55\u898b\u75be\u75c5\u7684\u6cbb\u7642\u548c\u57fa\u56e0\u79d1\u6280\u7684\u767c\u5c55\uff0c\u9700\u8981\u57fa\u56e0\u79d1\u6280\u5c08\u696d\u5718\u968a\uff0c\u548c\u5168\u793e\u6703\u7684\u95dc\u6ce8\u548c\u53c3\u8207\u3002\u53ea\u6709\u5171\u540c\u52aa\u529b\uff0c\u624d\u80fd\u5be6\u73fe\u66f4\u591a\u60a3\u8005\u7684\u5eb7\u5fa9\u548c\u5065\u5eb7\u3002<\/p>\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-full is-resized\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"1024\" src=\"https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/2.jpg\" alt=\"\" class=\"wp-image-3484\" style=\"width:840px;height:auto\" srcset=\"https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/2.jpg 1024w, https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/2-300x300.jpg 300w, https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/2-150x150.jpg 150w, https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/2-768x768.jpg 768w, https:\/\/imbhg.tcu.edu.tw\/wp-content\/uploads\/2024\/03\/2-375x375.jpg 375w\" sizes=\"auto, (max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n<\/div>\n\n\n<p class=\"wp-block-paragraph\">\u8cc7\u6599\u4f86\u6e90:<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">\u4ec0\u9ebc\u662f\u810a\u9ad3\u808c\u8089\u840e\u7e2e\u75c7?<\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><a href=\"https:\/\/www.taiwansma.org.tw\/?.p=HjEL\">https:\/\/www.taiwansma.org.tw\/?.p=HjEL<\/a><\/p>\n\n\n\n<p class=\"wp-block-paragraph\">\u300c\u5168\u7403\u6700\u8cb4\u85e5\u5291\u300d8\u6708\u5c07\u7d0d\u4fdd\uff01\u4e00\u52914900\u842c \u6210\u5065\u4fdd\u53f2\u4e0a\u6700\u8cb4\u7d66\u4ed8\u85e5\u7269<\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><a href=\"https:\/\/reurl.cc\/orb2gD\">https:\/\/reurl.cc\/orb2gD<\/a><\/p>\n\n\n\n<p class=\"wp-block-paragraph\">\u62531\u52914900\u842c\uff01\u300c\u5168\u7403\u6700\u8cb4\u7f55\u75c5\u85e5\u300d\u8afe\u5065\u751f8\u6708\u5c07\u7d0d\u5065\u4fdd\uff0c\u4ed8\u5929\u50f9\u6709\u7406\uff1f\u5065\u4fdd\u7f72\u9ede\u51fa\u8003\u91cf\u95dc\u9375<\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><a href=\"https:\/\/www.businesstoday.com.tw\/article\/category\/183027\/post\/202307210017\/\">https:\/\/www.businesstoday.com.tw\/article\/category\/183027\/post\/202307210017\/<\/a><\/p>\n\n\n\n<p class=\"wp-block-paragraph\">\u53f2\u4e0a\u6700\u8cb4\uff01\u4e00\u5291\u65b0\u53f0\u5e636000\u842c\uff01\u4e00\u91dd\u898b\u6548\u795e\u5947\u5728\u54ea\uff1f\u57fa\u56e0\u6cbb\u7642\u85e5\u7269\u8afe\u5065\u751f\uff0c\u5982\u4f55\u5c0d\u6297SMA\u810a\u9ad3\u6027\u808c\u8089\u840e\u7e2e\u75c7\uff1f<\/p>\n\n\n\n<figure class=\"wp-block-embed is-type-video is-provider-youtube wp-block-embed-youtube wp-embed-aspect-16-9 wp-has-aspect-ratio\"><div class=\"wp-block-embed__wrapper\">\n<iframe loading=\"lazy\" title=\"\u53f2\u4e0a\u6700\u8cb4\uff01\u4e00\u5291\u65b0\u53f0\u5e636000\u842c\uff01\u4e00\u91dd\u898b\u6548\u795e\u5947\u5728\u54ea\uff1f\u57fa\u56e0\u6cbb\u7642\u85e5\u7269\u8afe\u5065\u751f\uff0c\u5982\u4f55\u5c0d\u6297SMA\u810a\u9ad3\u6027\u808c\u8089\u840e\u7e2e\u75c7\uff1f\" width=\"900\" height=\"506\" src=\"https:\/\/www.youtube.com\/embed\/lNdJq_4Dtx0?feature=oembed\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; 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title=\"\u5206\u907a\u7cfb\u7f55\u898b\u75be\u75c5\u5ba3\u5c0e\u6f14\u8b1b\u7cfb\u5217-\u7f79\u60a3\u907a\u50b3\u75be\u75c5\u5bb6\u5ead\u7684\u751f\u547d\u56f0\u5883\u8207\u51fa\u8def &#8212; \u5206\u5b50\u751f\u7269\u66a8\u4eba\u985e\u907a\u50b3\u5b78\u7cfb\" src=\"https:\/\/imbhg.tcu.edu.tw\/?p=1511&#038;embed=true#?secret=WEDqncRHFj#?secret=FXK6pW3iSW\" data-secret=\"FXK6pW3iSW\" width=\"600\" height=\"338\" frameborder=\"0\" marginwidth=\"0\" marginheight=\"0\" scrolling=\"no\"><\/iframe>\n<\/div><\/figure>\n\n\n\n<p class=\"wp-block-paragraph\">\u7f55\u75c5\u60a3\u8005\u6797\u5b50\u671f\u5713\u6eff7\u5929\u5927\u5b78\u751f\u6d3b\u5922<\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><a href=\"https:\/\/www.tfrd.org.tw\/tfrd\/library_d\/content\/id\/1590\">https:\/\/www.tfrd.org.tw\/tfrd\/library_d\/content\/id\/1590<\/a><\/p>\n\n\n\n<p class=\"wp-block-paragraph\">\u5168\u7403\u7f55\u75c5\u7814\u7a76\u8cfd\u3000\u6148\u6fdf\u5927\u5b78\u596a\u9280<\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><a href=\"https:\/\/www.tfrd.org.tw\/tfrd\/library_d\/content\/id\/1875\">https:\/\/www.tfrd.org.tw\/tfrd\/library_d\/content\/id\/1875<\/a><\/p>\n","protected":false},"excerpt":{"rendered":"<p>\u5716\/\u6587 \u5f35\u65b0\u4faf\u6559\u6388 \u62531\u529149000\u842c\uff01\u5168\u7403\u6700\u8cb4\u85e5\u7269\u4e4b\u4e00\u300c\u8afe\u5065\u751f\u300d (Zolgensma)\uff0c\u6cbb\u7642\u7f55\u898b&#8230;<\/p>\n<p class=\"continue-reading-button\"> <a class=\"continue-reading-link\" href=\"https:\/\/imbhg.tcu.edu.tw\/?p=3480\">Continue reading<i 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